Dyke-Davidoff-Masson syndrome.
نویسندگان
چکیده
Dyke Davidoff Masson syndrome (DDMS) is characterized by seizures, facial asymmetry, contralateral hemiplegia and mental retardation. The characteristic radiologic features are cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. We report a case of DDMS in an 18-month-old girl who presented with right sided focal seizures, hemiparesis of the same side, and delayed milestones.
منابع مشابه
Dyke-Davidoff-Masson Syndrome: An Uncommon Cause of Refractory Epilepsy Identifyied by Neuro-Imaging
Refractory epilepsy is common in practice of neurology. Dyke-Davidoff-Masson Syndrome (DDMS) is one among the syndromes associated with refractory epilepsy. We have come across a case of Dyke-Davidoff-Masson syndrome while investigating a case of refractory epilepsy. When cerebral hemi atrophy is associated with the radiological features of osseous hypertrophy of calvarium, hyper-pneumatisation...
متن کاملDyke–Davidoff–Masson syndrome in a Nigerian
Dyke-Davidoff-Masson syndrome (DDMS) is a rare, but important cause of drug-resistant seizures. Dyke-Davidoff-Masson syndrome is a constellation of clinical features that consists of hemiparesis, seizure, facial asymmetry, and intellectual disability with distinct neuroimaging features. A 27-year-old lady presented to us with drug-resistant epilepsy, hemiparesis, and intellectual disability tha...
متن کاملDyke-Davidoff-Masson syndrome: case report of fetal unilateral ventriculomegaly and hypoplastic left middle cerebral artery
Prenatal ultrasonographic detection of unilateral cerebral ventriculomegaly arises suspicion of pathological condition related to cerebrospinal fluid flow obstruction or cerebral parenchimal pathology. Dyke-Davidoff-Masson syndrome is a rare condition characterized by cerebral hemiatrophy, calvarial thickening, skull and facial asymmetry, contralateral hemiparesis, cognitive impairment and seiz...
متن کاملA rare cause for seizures and mental retardation – Dyke Davidoff Masson Syndrome
Cerebral hemiatrophy Diagnosed Homolateral hypertrophy Dyke – Davidoff – Masson Syndrome (DDMS), also called as cerebral hemiatrophy, is a rare clinical condition characterized by seizures, facial asymmetry, contralateral spastic hemiplegia or hemiparesis, with learning difficulties. It is commonly diagnosed in presence of associated radiologic findings which include cerebral hemiatrophy with h...
متن کاملDyke-Davidoff-Masson Syndrome--Revisited.
the right side. All the findings favoured diagnosis of Dyke David -Masson syndrome. Significant contrasting feature in our patient than the patient described in the journal was the presence of left sided cerebellar atrophy (Figure 1). DykeDavidoff-Masson syndrome associated with crossed cerebellar atrophy (CCA) has been previously described in some pat ients . There are two schools of thought r...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
- Indian pediatrics
دوره 45 11 شماره
صفحات -
تاریخ انتشار 2008